DOCTORATE in GENETICS, ONCOLOGY and CLINICAL MEDICINE (GenOMeC)
DOTTORATO DI RICERCA IN GENETICA ONCOLOGIA E MEDICINA CLINICA

UNIVERSITA' DEGLI STUDI  DI SIENA

                                                                                        Home Page

 

Publications from 2005 to 2010

 
ARIANI FRANCESCA
 
  • PARRI V, KATZAKI E, ULIANA V, SCIONTI F, TITA R, ARTUSO R, LONGO I, BOSCHLOO R, VIJZELAAR R, SELICORNI A, BRANCATI F, DALLAPICCOLA B, ZELANTE L, HAMEL CP, SARDA P, LALANI SR, GRASSO R, BUONI S, HAYEK J, SERVAIS L, DE VRIES BB, GEORGOUDI N, NAKOU S, PETERSEN MB, MARI F, RENIERI A, ARIANI F. (2010). High frequency of COH1 intragenic deletions and duplications detected by MLPA in patients with Cohen syndrome. EUROPEAN JOURNAL OF HUMAN GENETICS, vol. 18; p. 1133-1140, ISSN: 1018-4813
  • ULIANA V, GROSSO S, CIONI M, ARIANI F., PAPA FT, TAMBURELLO S, ROSSI E, KATZAKI E, MUCCIOLO M, MAROZZA A, POLLAZZON M, MENCARELLI MA, MARI F, BALESTRI P, RENIERI A (2010). 3.2 Mb microdeletion in chromosome 7 bands q22.2-q22.3 associated with overgrowth and delayed bone age. EUROPEAN JOURNAL OF MEDICAL GENETICS, vol. 53; p. 168-170, ISSN: 1769-7212
  • CASELLI R, MENCARELLI MA, PAPA FT, ARIANI F., LONGO I, MELONI I, VONELLA G, ACAMPA M, AUTERI A, VICARI S, ORSI A, HAYEK G, RENIERI A, MARI F (2008). Delineation of the phenotype associated with 7q36.1q36.2 deletion: long QT
    syndrome, renal hypoplasia and mental retardation. AMERICAN JOURNAL OF MEDICAL GENETICS. PART A, vol. 146A; p. 1195-1199, ISSN: 1552-4825
  • SAMPIERI K, AMENDUNI M, PAPA FT, KATZAKI E, MENCARELLI MA, MAROZZA A, EPISTOLATO, MC, TOTI P, LAZZI S, BRUTTINI M, DE FILIPPIS R, DE FRANCESCO S, LONGO I, MELONI I, MARI F, ACQUAVIVA A, HADJISTILIANOU T, RENIERI A, ARIANI F. (2009). Array comparative genomic hybridization in retinoma and retinoblastoma tissues. CANCER SCIENCE, ISSN: 1347-9032
  • ARIANI F., HAYEK G, RONDINELLA D, ARTUSO R, MENCARELLI MA, SPANHOL-ROSSETO A, POLLAZZON M, BUONI S, SPIGA O, RICCIARDI S, MELONI I, LONGO I, MARI F, BROCCOLI, V, ZAPPELLA M, RENIERI A (2008). FOXG1 is responsible for the congenital variant of Rett syndrome. AMERICAN JOURNAL OF HUMAN GENETICS, vol. 83; p. 89-93, ISSN: 0002-9297
  • PAPA FT, MENCARELLI MA, CASELLI R, KATZAKI E, SAMPIERI K, MELONI I, ARIANI F., LONGO I, MAGGIO A, BALESTRI P, GROSSO S, FARNETANI MA, BERARDI R, MARI F, RENIERI A (2008). A 3 Mb deletion in 14q12 causes severe mental retardation, mild facial
    dysmorphisms and Rett-like features. AMERICAN JOURNAL OF MEDICAL GENETICS. PART A, vol. 146A; p. 1994-1998, ISSN: 1552-4825
  • RENIERI A, MARI F, MENCARELLI MA, SCALA E, ARIANI F., LONGO I, MELONI I, CEVENINI G, PINI G, HAYEK G, ZAPPELLA M (2008). Diagnostic criteria for the Zappella variant of Rett syndrome (the preserved
    speech variant). BRAIN & DEVELOPMENT, ISSN: 0387-7604
  • SAMPIERI K, MENCARELLI MA, CARMELA EPISTOLATO M, TOTI P, LAZZI S, BRUTTINI M, DE FRANCESCO S, LONGO I, MELONI I, MARI F, ACQUAVIVA A, HADJISTILIANOU T, RENIERI A, ARIANI F. (2008). Genomic differences between retinoma and retinoblastoma. ACTA ONCOLOGICA, vol. 47; p. 1483-1492, ISSN: 0284-186X
  • MENCARELLI MA, KATZAKI E, PAPA FT, SAMPIERI K, CASELLI R, ULIANA V, POLLAZZON M, CANITANO R, MOSTARDINI R, GROSSO S, LONGO I, ARIANI F., MELONI I, HAYEK J, BALESTRI P, MARI F, RENIERI A (2008). Private inherited microdeletion/microduplications: implications in clinical
    practice. EUROPEAN JOURNAL OF MEDICAL GENETICS, vol. 51; p. 409-416, ISSN: 1769-7212
  • MELONI I, PARRI V, DE FILIPPIS R, ARIANI F., ARTUSO R, BRUTTINI M, KATZAKI E, LONGO I, MARI F, BELLAN C, DOTTI CG, RENIERI A (2008). The XLMR gene ACSL4 plays a role in dendritic spine architecture. NEUROSCIENCE, ISSN: 0306-4522
  • ARTUSO R, MENCARELLI MA, POLLI R, SARTORI S, ARIANI F., POLLAZZON M, MAROZZA A, CILIO MR, SPECCHIO N, VIGEVANO F, VECCHI M, BONIVER C, BERNARDINA BD, PARMEGGIANI A, BUONI S, HAYEK G, MARI F, RENIERI A, MURGIA A (2009). Early-onset seizure variant of Rett syndrome: Definition of the clinical diagnostic criteria. BRAIN & DEVELOPMENT, ISSN: 0387-7604
  • MAKRYTHANASIS P, KAPRANOV P, BARTOLONI L, REYMOND A, DEUTSCH S, GUIGÓ R, DENOEUD F, DRENKOW J, ROSSIER C, ARIANI F., CAPRA V, EXCOFFIER L, RENIERI A, GINGERAS TR, ANTONARAKIS SE (2009). Variation in novel exons (RACEfrags) of the MECP2 gene in Rett syndrome patients and controls. HUMAN MUTATION, vol. 30, ISSN: 1059-7794
  • MENCARELLI M, SPANHOL-ROSSETO A, ARTUSO R, RONDINELLA D, DE FILIPPIS R, BAHI-BUISSON N, NECTOUX J, RUBINSZTAJN R, BIENVENU T, MONCLA A, CHABROL B, VILLARD L, KRUMINA Z, ARMSTRONG J, ROCHE A, PINEDA M, GAK E, MARI F, ARIANI F., RENIERI A (2009). Novel FOXG1 mutations associated with the congenital variant of Rett syndrome. JOURNAL OF MEDICAL GENETICS, vol. ?, ISSN: 0022-2593
  • MENCARELLI MA, KLEEFSTRA T, KATZAKI E, PAPA FT, COHEN M, PFUNDT R, ARIANI F., MELONI I, MARI F, RENIERI A (2009). 14q12 Microdeletion syndrome and congenital variant of Rett syndrome. EUROPEAN JOURNAL OF MEDICAL GENETICS, vol. 52; p. 148-152, ISSN: 1769-7212
  • ULIANA V, GIORDANO N, CASELLI R, PAPA FT, ARIANI F., MARCOCCI C, GIANETTI E, MARTINI G, PAPAKOSTAS P, ROLLO F, MELONI I, MARI F, PRIOLO M, RENIERI A, NUTI R (2008). Expanding the phenotype of 22q11 deletion syndrome: the MURCS association. CLINICAL DYSMORPHOLOGY, vol. 17; p. 13-17, ISSN: 0962-8827
  • SCALA E, ARIANI F., MARI F, CASELLI R, PESCUCCI C, LONGO I, MELONI I, GIACHINO D, BRUTTINI M, HAYEK G, ZAPPELLA M, RENIERI A (2005). CDKL5/STK9 is mutated in Rett syndrome variant with infantile spasms. JOURNAL OF MEDICAL GENETICS, vol. 42 (2); p. 103-107, ISSN: 0022-2593
  • CASELLI R, MENCARELLI MA, PAPA FT, ULIANA V, SCHIAVONE S, STRAMBI M, PESCUCCI C, ARIANI F., ROSSI V, LONGO I, MELONI I, RENIERI A, MARI F (2007). A 2.6 Mb deletion of 6q24.3-25.1 in a patient with growth failure, cardiac septal defect, thin upperlip and asymmetric dysmorphic ears. EUROPEAN JOURNAL OF HUMAN GENETICS, vol. 50(4); p. 315-321, ISSN: 1018-4813
  • KATZAKI E, PESCUCCI C, ULIANA V, PAPA FT, ARIANI F., MELONI I, PRIOLO M, SELICORNI A, MILANI D, FISCHETTO R, CELLE ME, GRASSO R, DALLAPICCOLA B, BRANCATI F, BORDIGNON M, TENCONI R, FEDERICO A, MARI F, RENIERI A, LONGO I (2007). Clinical and molecular characterization of Italian patients affected by Cohen
    syndrome. JOURNAL OF HUMAN GENETICS, vol. 52; p. 1011-1017, ISSN: 1435-232X
  • MICHELI V, SESTINI S, PARRI V, FICHERA M, ROMANO C, ARIANI F., LONGO I, MARI F, BRUTTINI M, RENIERI A, MELONI I (2007). RSK2 enzymatic assay as a second level diagnostic tool in Coffin-Lowry syndrome. CLINICA CHIMICA ACTA, vol. 384(1-2); p. 35-40, ISSN: 0009-8981
  • PESCUCCI C, CASELLI R, MARI F, SPECIALE C, ARIANI F., BRUTTINI M, SAMPIERI K, MENCARELLI MA, SCALA E, LONGO I, ARTUSO R, RENIERI A, MELONI I, XLMR ITALIAN NETWORK (2007). The Italian XLMR bank: a clinical and molecular database. HUMAN MUTATION, vol. 28(1); p. 13-18, ISSN: 1059-7794
  • MARI F, GIACHINO D, RUSSO L, PILIA G, ARIANI F., SCALA E, CHIAPPE F, SAMPIERI K, CAPOROSSI A, RENIERI A, LASORELLA G (2006). Blepharophimosis, ptosis, and epicanthus inversus syndrome: clinical and molecular analysis of a case. JOURNAL OF AAPOS, vol. 10(3); p. 279-280, ISSN: 1091-8531
  • SCALA E, LONGO I, OTTIMO F, SPECIALE C, SAMPIERI K, KATZAKI E, ARTUSO R, MENCARELLI MA, D'AMBROGIO T, VONELLA G, ZAPPELLA M, HAYEK G, BATTAGLIA A, MARI F, RENIERI A, ARIANI F. (2007). MECP2 deletions and genotype-phenotype correlation in Rett syndrome. AMERICAN JOURNAL OF MEDICAL GENETICS. PART A, vol. 143A; p. 2775-2784, ISSN: 1552-4825
  • SQUILLARO T, CAMBI F, CIACCI G, ROSSI S, ULIVELLI M, MALANDRINI A, MENCARELLI MA, MARI F, RENIERI A, ARIANI F. (2007). Frequency of the LRRK2 G2019S mutation in Italian patients affected by Parkinson's disease. JOURNAL OF HUMAN GENETICS, vol. 52(3); p. 201-204, ISSN: 1435-232X
  • SAMPIERI K, MELONI I, SCALA E, ARIANI F., CASELLI R, PESCUCCI C, LONGO I, ARTUSO R, BRUTTINI M, MENCARELLI MA, SPECIALE C, CAUSARANO V, HAYEK G, ZAPPELLA M, RENIERI A, MARI F (2007). Italian Rett database and biobank. HUMAN MUTATION, vol. 28(4); p. 229-235, ISSN: 1059-7794
  • ARIANI F., LONGO I, FREZZOTTI P, PESCUCCI C, MARI F, CAPOROSSI A, FREZZOTTI R, RENIERI A (2006). Optineurin gene is not involved in the common high-tension form of primary open-angle glaucoma. GRAEFE'S ARCHIVE FOR CLINICAL AND EXPERIMENTAL OPHTHALMOLOGY, vol. 244(9); p. 1077-1082, ISSN: 0721-832X
  • MARI F, AZIMONTI S, BERTANI I, BOLOGNESE F, COLOMBO E, CASELLI R, SCALA E, LONGO I, GROSSO S, PESCUCCI C, ARIANI F., HAYEK G, BALESTRI P, BERGO A, BADARACCO G, ZAPPELLA M, BROCCOLI V, RENIERI A, KILSTRUP-NIELSEN C, LANDSBERGER N (2005). CDKL5 belongs to the same molecular pathway of MeCP2 and it is responsible for the early-onset seizure variant of Rett syndrome. HUMAN MOLECULAR GENETICS, vol. 14 (14); p. 1935-1946, ISSN: 0964-6906
  • MARI F, CASELLI R, RUSSO S, COGLIATI F, ARIANI F., LONGO I, BRUTTINI M, MELONI I, PESCUCCI C, SCHURFELD K, TOTI P, TASSINI M, LARIZZA L, HAYEK G, ZAPPELLA M, RENIERI A (2005). Germline mosaicism in Rett syndrome identified by prenatal diagnosis. CLINICAL GENETICS, vol. 67(3); p. 258-260, ISSN: 0009-9163
  • RENIERI A, PESCUCCI C, LONGO I, ARIANI F., MARI F, MELONI I (2005). Non-syndromic X-linked mental retardation: from a molecular to a clinical point of view. JOURNAL OF CELLULAR PHYSIOLOGY, vol. 204(1); p. 8-20, ISSN: 0021-9541
  •